Scimitar syndrome is a rare, congenital malformation, characterized by the partial or total anomalous pulmonary venous return from the right lung. It can present as early as in neonatal period or incidentally later in life. We report the case of a 41-year-old female, with Hypertension and diabetes, who was diagnosed with Scimitar syndrome after examinations for recurrent wheezing and cough.
Echocardiography showed increased flow in the inferior vena cava, without a cardiac abnormality. The chest radiograph showed a scimitar sign in the right hemithorax, obscuring the contours of the right atrium.The diagnosis was confirmed by tomodensitometry.
The patient undergoing cardiac catheterization for radiographic and hemodynamic evaluations to obtain a broad evaluation of the complex cardiac anatomy in this case, and to search for concomitant congenital heart diseases.However, CT scan or magnetic resonance imaging (MRI) has more sensitivity and specificity for this diagnosis and gives more anatomical information before surgical correction.We are waiting for the results actually.Adult patients typically remain asymptomatic and are incidentally discovered. Some adult patients may present with symptoms of fatigue, dyspnea, or recurrent pneumonia. Most patients with isolated Scimitar syndrome have excellent prognosis. 20201104_174441.mp4
Scimitar syndrome is occasionally seen in adults characterized by minimal symptoms. Imaging techniques including Echocardiography, conventional X-ray, computed tomography, MRI are necessary to confirm the diagnosis or visualize the associated anomalies.